Dravet syndrome is a rare epileptic encephalopathy classified in 1989 by the International League Against Epilepsy (ILAE) as a “syndrome undetermined as to whether seizures are focal or generalized” and more recently as a “genetic and developmental epilepsy syndrome with onset in infancy.”
Incidence has been estimated at between 1/16,000 and 1/21,000. For population projections, an estimate using birth rates can be used. For example, if an area has a birth rate of about 210,000 per year, it would be estimated that about 10 babies would be born each year with Dravet syndrome.
One of the goals of the IICEPR(International Ion Channel Epilepsy Patient Registry) is to establish a more accurate count of patients worldwide who have Dravet syndrome and related ion channel epilepsies.
- Wu et al. “Incidence of Dravet Syndrome in a U.S. Population,” Pediatrics, October 5, 2015, pii: peds.2015-1807
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